Ataxia-Deafness-Retardation Syndrome is a rare genetic syndrome characterized by intellectual disability, deafness, ataxia, developmental delay and progressive sensorineural hearing loss. It is different from the Richards-Rundle syndrome, although both share the ataxia, deafness, and intellectual disability. The condition shows an autosomal recessive pattern of inheritance. However, one of the studies has also suggested X-linked inheritance as a possible inheritance pattern.