Teebi type hypertelorism is an autosomal dominant disorder which is differentiated from other types of hypertelorism by the numerous correlated dysmorphic craniofacial characteristics that might or might not be present in all patients. Those features include prominent forehead, downslanting long palpebral fissures, depressed nasal bridge, broad nasal tip, long philtrum, heavy and broad eyebrows, anterior hair implantation coinciding a widow's peak, neonatal teeth, thin upper lip, everted lower lip, small chin, low-set ears, preauricular fistulas and short neck. Teebi type hypertelorism has been described only in 20 patients so far belonging to five diverse families. Various eye abnormalities were portrayed in patients comprising ptosis (occasionally requires surgical correction), mild exophthalmos, and iridochorioretinal colobomas. It varies from craniofrontonasal dysplasis by a nasal tip that might appear to be broad but not bifid, normal stature, and the lack of craniosynostosis or anomalies of the fingernails. This disorder appears during infancy with a prevalence of <1/1000,000.