Hyperphosphatasia with Impaired Intellectual Development Syndrome 2

Alternative Names

  • HPMRS2
  • Glycosylphosphatidylinositol Biosynthesis Defect 6
  • GPIBD6
Back to search Result
WHO-ICD-10 version:2010

Congenital malformations, deformations and chromosomal abnormalities

Other congenital malformations

OMIM Number

614749

Mode of Inheritance

Autosomal recessive

Gene Map Locus

9p13.3

Description

Hyperphosphatasia with impaired intellectual development syndrome-2 (HPMRS2) is an autosomal recessive disorder characterized by moderately to severely delayed psychomotor development, facial dysmorphism, brachytelephalangy, and increased serum alkaline phosphatase (hyperphosphatasia). Some patients may have additional features, such as cardiac septal defects or seizures. The disorder is caused by a defect in glycosylphosphatidylinositol (GPI) biosynthesis. [From OMIM]

Epidemiology in the Arab World

View Map
Subject IDCountrySexFamily HistoryParental ConsanguinityHPO TermsVariantZygosityMode of InheritanceReferenceRemarks
614749.1.1TunisiaFemaleYesYes Elevated circulating alkaline phosphatas...NM_032634.4:c.1132C>THomozygousAutosomal, RecessiveAguech et al. 2023 Patient has a family...
© CAGS 2025. All rights reserved.